Zych-Twardowska Elzbieta, Wajgt Andrzej, Lubos Leszek, Matusik Edyta
Katedra i Klinika Neurologii Slaskiej AM w Katowicach.
Neurol Neurochir Pol. 2003;37 Suppl 5:189-96.
We are presenting a case of Parkinson-ALS-Dementia complex in 53 years old male. Outstanding bulbar signs with muscular atrophy of tongue, muscular atrophy of shoulder girdle together with massive fasciculations (myoclonus type descending from spinal cord) have been observed. Clear Parkinson's syndrome coexisted--bradykinesia, rigidity with cogwheel resistance, "masking" of the face, disturbances of body balance and significant vegetative signs. Moreover psychological testing has shown psycho-organic syndrome of frontal type, MRI scans proved the existence of slight brain general atrophy that is most prominent in frontal et temporal poles. Diseases of this kind occur all over the world sporadically. The case of ALS--dementia complex was observed in our clinic a year ago.
我们报告一例53岁男性的帕金森-肌萎缩侧索硬化症-痴呆综合征。观察到明显的延髓体征，伴有舌肌萎缩、肩胛带肌萎缩以及大量肌束震颤（脊髓源性肌阵挛型）。同时存在明确的帕金森综合征——运动迟缓、齿轮样强直、面部“面具样”表现、身体平衡障碍以及明显的自主神经症状。此外，心理测试显示为额叶型精神器质性综合征，MRI扫描证实存在轻度脑萎缩，以额颞叶极最为明显。这类疾病在世界各地均有散发病例。一年前我们诊所曾观察到一例肌萎缩侧索硬化症-痴呆综合征病例。
