Bozdağ Kübra Eren, Biçakçi Hülya, Ermete Murat
Department of Dermatology and Pathology, Atatürk Research and Training Hospital, Izmir, Turkey.
Int J Dermatol. 2004 Jul;43(7):518-20. doi: 10.1111/j.1365-4632.2004.02158.x.
Porokeratosis is a disorder of keratinization characterized by annular plaques with an atrophic center surrounded by a raised, keratotic wall. It has several clinical forms including a porokeratosis of Mibelli, giant porokeratosis, linear porokeratosis, disseminated superficial actinic porokeratosis, palmoplantar porokeratosis and punctate porokeratosis. We report a patient with the rare condition of giant porokeratosis. Several variants of porokeratosis coexist in our patient.
汗孔角化症是一种角化异常性疾病,其特征为环形斑块,中心萎缩,周围有隆起的角化性边缘。它有多种临床类型,包括米贝利汗孔角化症、巨大汗孔角化症、线状汗孔角化症、播散性浅表性光化性汗孔角化症、掌跖汗孔角化症和点状汗孔角化症。我们报告了1例患有罕见的巨大汗孔角化症的患者。在我们的患者中,多种汗孔角化症变体同时存在。