Finidori G, Rigault P, Padovani J P, Naouri A
Rev Chir Orthop Reparatrice Appar Mot. 1978 Jul-Aug;64(5):367-74.
Hemimelica Epiphysialis Dysplasia is a rare osteochondrodystrophy producing cartilaginous epiphysial hypertrophy with hemimelic topography involving preferentialy the lower limb. Lesions are generally medialy situated (medial condyle of the femur, medial malleolus talus, tarsal scaphoid and first metatarsal bone). 8 cases of patients are discussed with a follow up of 4 years. The evolution is to a massive ossification of the hypertrophic cartilaginous areas. The issue is a fast arthrosic degeneration of the involved joints (mainly the ankle, more rarely the knee). The surgical procedures are often unsuccessful.
半侧骨骺发育异常是一种罕见的骨软骨发育不良,表现为软骨性骨骺肥大,具有半侧肢体形态,主要累及下肢。病变通常位于内侧(股骨内侧髁、距骨内侧踝、舟状骨和第一跖骨)。讨论了8例患者,随访4年。病变发展为肥大软骨区域的大量骨化。问题是受累关节(主要是踝关节,较少见膝关节)迅速出现关节退变。手术治疗往往不成功。