Azouz E M, Slomic A M, Marton D, Rigault P, Finidori G
Pediatr Radiol. 1985;15(1):44-9. doi: 10.1007/BF02387852.
Dysplasia epiphysealis hemimelica (DEH) is an osteocartilaginous overgrowth involving one or multiple epiphyses or ossification centers, usually in a lower extremity on one side of the body. Characteristically the involvement is hemimelic i.e. either the medial or lateral part of the ossification center is involved. We have studied 24 patients with DEH and are adding 15 new cases to the literature. Because of the variable manifestations of the dysplasia and its different degrees of involvement in the affected children, we have subdivided it into localized, classical and generalized forms. In the generalized form, there is involvement of a whole lower extremity from the pelvis to the foot, and some of these patients show megaepiphyses with enlargement of a whole epiphyseal center, not only its medial or lateral part. We have also described and illustrated other special features of the dysplasia especially the advanced bone age and the metaphyseal and growth plate involvement.
骨骺半侧发育不良（DEH）是一种骨软骨过度生长，累及一个或多个骨骺或骨化中心，通常发生在身体一侧的下肢。其特征性表现为半侧受累，即骨化中心的内侧或外侧部分受累。我们研究了24例DEH患者，并在文献中新增了15例病例。由于该发育不良的表现多样，且在受影响儿童中的受累程度不同，我们将其细分为局限性、典型性和全身性三种类型。在全身性类型中，整个下肢从骨盆到足部均受累，其中一些患者表现为巨骨骺，整个骨骺中心增大，不仅是其内侧或外侧部分。我们还描述并举例说明了该发育不良的其他特殊特征，尤其是骨龄提前以及干骺端和生长板受累情况。
