Griffiths S J, Tang W, Parameswaran R, Kelsey A, West C G H
Department of Neurosurgery, Royal Manchester Children's Hospital, Pendlebury, Manchester, UK.
Br J Neurosurg. 2004 Jun;18(3):293-7. doi: 10.1080/02688690410001732788.
A 9-year-old boy presented with a 12-month history of headaches and recent grand mal seizures. Computed tomography and magnetic resonance imaging of the brain revealed an enhancing right frontal convexity lesion. The preoperative diagnosis was meningioma. However, histological examination was diagnostic of Rosai-Dorfman disease. Rosai-Dorfman disease confined to the intracranial compartment is very rare, of 34 reported cases only one presented in the first decade. Optimal treatment has not been established, but complete surgical resection alone seems effective and allows histological distinction from meningioma.
一名9岁男孩有12个月的头痛病史，近期出现癫痫大发作。脑部计算机断层扫描和磁共振成像显示右侧额叶凸面有一个强化病灶。术前诊断为脑膜瘤。然而，组织学检查诊断为罗萨伊-多夫曼病。局限于颅内的罗萨伊-多夫曼病非常罕见，在34例报告病例中，只有1例发生在第一个十年。尚未确定最佳治疗方法，但单纯完整手术切除似乎有效，且能从组织学上与脑膜瘤区分开来。
