Brodsky R A, Jones R J
The Sidney Kimmel Comprehensive Cancer Center at Johns Hopkins, Baltimore, MD, USA.
Leukemia. 2004 Oct;18(10):1740-2. doi: 10.1038/sj.leu.2403487.
Secondary myelodysplastic syndrome (MDS)/acute leukemia frequently evolves from severe aplastic anemia (SAA) following immunosuppressive therapy. Secondary clonal cytogenetic abnormalities have now been reported after noncytotoxic therapy in two additional settings: all trans retinoic acid (ATRA) treatment of acute promyelocytic leukemia (APL) and imatinib for chronic myeloid leukemia (CML). We propose that SAA, APL, CML, and MDS represent different manifestations of generalized insults to the bone marrow. In SAA, the insult to hematopoietic progenitors leads to an immune attack, while in APL, CML, and MDS, it gives rise to the malignant clones. A primary insult to bone marrow could simultaneously lead to several abnormal hematopoietic cell clones, with one dominating and the others present but below the level of detection. Such a 'field leukemogenic effect' would be analogous to the 'field cancerization effect' described in solid tumors. Nonspecific cytotoxic therapies, including antileukemic chemotherapy and allogeneic transplantation, have broad activity that could inhibit both the overt disease and other undetectable coexistent abnormal clones. In contrast, disease-specific targeted therapy such as immunosuppressive therapy in aplastic anemia, ATRA in APL, or imatinib in CML would have no activity against other abnormal clones, allowing them to expand and become detectable as the dominant clone declines.
继发性骨髓增生异常综合征(MDS)/急性白血病常继发于免疫抑制治疗后的重型再生障碍性贫血(SAA)。现已报道在另外两种情况下非细胞毒性治疗后出现继发性克隆性细胞遗传学异常:全反式维甲酸(ATRA)治疗急性早幼粒细胞白血病(APL)以及伊马替尼治疗慢性粒细胞白血病(CML)。我们提出,SAA、APL、CML和MDS代表了对骨髓的全身性损伤的不同表现形式。在SAA中,对造血祖细胞的损伤导致免疫攻击,而在APL、CML和MDS中,这种损伤则产生恶性克隆。对骨髓的原发性损伤可能同时导致多个异常造血细胞克隆,其中一个占主导地位,其他克隆虽然存在但低于检测水平。这种“场致白血病效应”类似于实体瘤中描述的“场癌化效应”。非特异性细胞毒性疗法,包括抗白血病化疗和异基因移植,具有广泛的活性,可抑制显性疾病和其他无法检测到的共存异常克隆。相比之下,疾病特异性靶向治疗,如再生障碍性贫血中的免疫抑制治疗、APL中的ATRA或CML中的伊马替尼,对其他异常克隆没有活性,随着显性克隆数量下降,这些异常克隆得以扩增并变得可检测到。