Porta A, Pierrottet C, Aschero M, Orzalesi N
San Paolo Hospital, Department of Ophthalmology, University of Milan, Italy.
Am J Ophthalmol. 1992 Feb 15;113(2):161-4. doi: 10.1016/s0002-9394(14)71528-4.
In two patients, we studied retinitis pigmentosa with preservation of the retinal pigment epithelium adjacent to and under the retinal arterioles (despite panretinal degeneration). Both patients with preserved para-arteriolar retinal pigment epithelium also exhibited a peculiarly strong hyperopia. In addition to previously reported features, these patients also had sheathing of the major vascular arcades, which suggested a vascular involvement in this uncommon form of retinitis pigmentosa.
在两名患者中，我们研究了视网膜色素变性，其视网膜色素上皮在视网膜小动脉旁及下方得以保留（尽管存在全视网膜变性）。两名视网膜小动脉旁视网膜色素上皮得以保留的患者也都表现出异常强烈的远视。除了先前报道的特征外，这些患者还存在主要血管弓的鞘膜形成，这提示在这种不常见的视网膜色素变性形式中存在血管受累情况。
