Atkinson J B, Foster C E, Lally K P, Isaacs H, Siegel S E
Division of Pediatric Surgery, Children's Hospital of Los Angeles, CA 90027.
J Pediatr Surg. 1992 Jan;27(1):105-7. doi: 10.1016/0022-3468(92)90120-v.
Extragonadal yolk sac tumors (YSTs) are uncommon and YSTs of the liver are exceedingly rare, with only three reported cases in the literature. A case is described of primary YST of the falciform ligament extending into the left lobe of the liver in a 14-month-old boy. This is the first reported case of primary YST arising within the falciform ligament. The patient underwent an exploratory laparotomy after presenting with hemoperitoneum. An extremely friable and necrotic tumor was found extending from the falciform ligament into the liver. The tumor was debulked and the patient received 5 months of chemotherapy employing a modified Einhorn regimen. After a partial response to chemotherapy the patient had a second-look laparotomy, at which time a left hepatic lobectomy and en bloc resection of the falciform ligament was performed in order to remove residual tumor. At the present time the patient has no signs of metastases and is alive and well 2 years after his presentation.
性腺外卵黄囊瘤（YSTs）并不常见，而肝脏的YSTs极为罕见，文献中仅报道过3例。本文描述了1例14个月大男孩，其镰状韧带原发性YST延伸至肝左叶。这是首次报道的起源于镰状韧带内的原发性YST病例。该患者因腹腔积血接受了剖腹探查术。发现一个极易碎且坏死的肿瘤从镰状韧带延伸至肝脏。肿瘤被大部切除，患者接受了5个月采用改良艾因霍恩方案的化疗。化疗出现部分缓解后，患者接受了二次剖腹探查术，此时进行了左肝叶切除术并整块切除镰状韧带，以切除残留肿瘤。目前，该患者没有转移迹象，自发病以来已存活2年且状况良好。
