Gan G G, Eow G I, Teh A, Ng S C, Sangkar J V
Department of Medicine, Faculty of Medicine, University of Malaya, 50603, Kuala Lumpur.
Med J Malaysia. 2004 Mar;59(1):100-2.
Familial hemophagocytic lymphohistiocytosis is a disorder which presents with fever, pancytopenia, liver dysfunction and also an increase in non-malignant histiocytes with prominent hemophagocytosis in various organs. It is usually difficult to distinguish from other hemophagocytic syndrome in the absence of family history. It rarely manifests in adults. Chemotherapy is usually indicated. Here, we report the occurrence of this disorder in two brothers in their twenties.
