King Robert S, Preston Glenn G, Berenberg Jeffrey L, Fraser Susan L, Gress Francis M
Department of Medicine, Tripler Army Medical Center, Honolulu, HI 96859, USA.
Hawaii Med J. 2004 Sep;63(9):262-3, 277.
A 36-year-old man with fever and pancytopenia due to Hemophagocytic Lymphohistiocytosis is reported. The patient was started on the HLH-94 based treatment. Two weeks after the initiation of therapy the patient's pancytopenia had resolved and he was discharged to complete treatment as an outpatient. The initial clinical presentation, diagnostic criteria, pathophysiology and treatment will be discussed.
报告了一名36岁因噬血细胞性淋巴组织细胞增生症导致发热和全血细胞减少的男性患者。该患者开始接受基于HLH - 94方案的治疗。治疗开始两周后,患者的全血细胞减少症得到缓解,随后出院作为门诊患者完成治疗。将对该患者的初始临床表现、诊断标准、病理生理学及治疗进行讨论。