Jimenez Juan Carlos, Emil Sherif, Podnos Yale, Nguyen Nam
Division of Pediatric Surgery, University of California, Irvine Medical Center, Orange, CA 92868-3298, USA.
J Pediatr Surg. 2004 Nov;39(11):1654-7. doi: 10.1016/j.jpedsurg.2004.07.003.
Annular pancreas is a recognized cause of duodenal obstruction in children. The authors sought to characterize the clinical, radiologic, and prognostic findings in this disorder through a 10-year review of all patients with annular pancreas.
A retrospective review of all annular pancreas cases identified between 1993 and 2002 at 2 tertiary pediatric surgical centers was completed. Factors analyzed included patient demographics, presenting symptoms, associated anomalies, radiologic findings, operation performed, postoperative outcomes, and complications.
Sixteen patients were identified. Four patients (25%) were premature. Twelve patients (75%) presented during the first week of life and the remainder within the first year. All patients presented with vomiting, which was nonbilious in 15 (94%). Five patients (31 %) had chromosomal anomalies, and 6 (38%) had other major congenital malformations. Eleven patients (69%) presented with partial duodenal obstruction. Operations performed were duodenoduodenostomy in 14 (88%), duodenojejunostomy in 1 (6%), and Ladd's procedure in 1 (6%). Enteral feedings were started, and full enteral feeding was achieved at an average of 8.4 days and 15.9 days after operation, respectively. All patients survived and were discharged after an average hospitalization of 24.0 days.
Patients with annular pancreas have preampullary duodenal obstruction, which is more commonly partial. Duodenoduodenostomy is the appropriate treatment. Prognosis is excellent, despite the frequent association with chromosomal anomalies and major congenital malformations.
环状胰腺是儿童十二指肠梗阻的一个公认病因。作者通过对所有环状胰腺患者进行为期10年的回顾,试图描述该疾病的临床、放射学及预后表现。
对1993年至2002年期间在两家三级儿科外科中心确诊的所有环状胰腺病例进行回顾性研究。分析的因素包括患者人口统计学资料、临床表现、相关畸形、放射学表现、实施的手术、术后结果及并发症。
共确定16例患者。4例(25%)为早产儿。12例(75%)在出生后第一周内出现症状,其余在第一年内出现。所有患者均有呕吐症状,其中15例(94%)呕吐物非胆汁性。5例(31%)有染色体异常,6例(38%)有其他主要先天性畸形。11例(69%)表现为十二指肠部分梗阻。实施的手术中,14例(88%)行十二指肠十二指肠吻合术,1例(6%)行十二指肠空肠吻合术,1例(6%)行拉德氏手术。术后分别平均在8.4天和15.9天开始肠内喂养并实现完全肠内喂养。所有患者均存活,平均住院24.0天后出院。
环状胰腺患者存在壶腹前十二指肠梗阻,多为部分性梗阻。十二指肠十二指肠吻合术是合适的治疗方法。尽管常伴有染色体异常和主要先天性畸形,但预后良好。