持久性斑状毛细血管扩张症伴发骨髓增殖性疾病。

Telangiectasia macularis eruptiva perstans with an associated myeloproliferative disorder.

作者信息

Martin Lucy K, Romanelli Paolo, Ahn Yeon Soong, Kirsner Robert S

机构信息

Department of Dermatology and Cutaneous Surgery, University of Miami School of Medicine, University of Miami, Miami, FL 33125, USA.

出版信息

Int J Dermatol. 2004 Dec;43(12):922-4. doi: 10.1111/j.1365-4632.2004.02249.x.

DOI:10.1111/j.1365-4632.2004.02249.x

PMID:15569020

Abstract

Telangiectasia macularis eruptiva perstans (TMEP) is a cutaneous form of mastocytosis. It has been rarely associated with an underlying myeloproliferative disorder. We report the case of a patient, while receiving treatment for thrombocytosis, with both platelet production and function inhibitors presented with TMEP. TMEP is often refractory to therapy; however, our patient responded to treatment with PUVA.

摘要

持久性斑状毛细血管扩张性肥大细胞增多症（TMEP）是肥大细胞增多症的一种皮肤表现形式。它很少与潜在的骨髓增殖性疾病相关。我们报告了一例患者，在接受血小板增多症治疗时，使用了血小板生成和功能抑制剂，出现了TMEP。TMEP通常对治疗难治；然而，我们的患者对补骨脂素紫外线A光化学疗法（PUVA）治疗有反应。