持久性斑状毛细血管扩张症经 PUVA 治疗后成功缓解。

Telangiectasia macularis eruptive perstans successfully treated with PUVA therapy.

机构信息

First Dermatologic Department, Medical School, Aristotle University, Thessaloniki, Greece.

出版信息

Photodermatol Photoimmunol Photomed. 2010 Feb;26(1):46-7. doi: 10.1111/j.1600-0781.2009.00480.x.

DOI:10.1111/j.1600-0781.2009.00480.x

PMID:20070840

Abstract

We present the case of a 58-year-old woman who was diagnosed as having telangiectasia macularis eruptiva perstans (TMEP) and was successfully treated with PUVA photochemotherapy. During the 6-month follow-up, no recurrence of pruritus or skin lesions was observed. TMEP represents a rare form of cutaneous mastocytosis, which is clinically characterized by reddish-brown telangiectatic macules symmetrically distributed over the trunk and extremities. Although in the majority of cases the disease is limited to the skin, systemic involvement may occur. The treatment of TMEP is challenging and several therapeutic modalities have been proposed in the past.

摘要

我们报告了一例 58 岁女性患者，该患者被诊断为持久性斑状毛细血管扩张性肥大细胞瘤（TMEP），并成功接受了 PUVA 光化学疗法治疗。在 6 个月的随访期间，未观察到瘙痒或皮肤损伤复发。TMEP 代表一种罕见的皮肤肥大细胞瘤形式，其临床特征为对称分布于躯干和四肢的红棕色毛细血管扩张性斑片。尽管在大多数情况下，该疾病仅限于皮肤，但也可能发生全身性受累。TMEP 的治疗具有挑战性，过去曾提出过多种治疗方法。