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以急性危及生命事件为表现的斯特奇-韦伯综合征。

Sturge-Weber syndrome presenting as an acute life-threatening event.

作者信息

Muñiz Antonio E

机构信息

Department of Emergency Medicine, Virginia Commonwealth University Medical Center, Richmond 23298-0401, USA.

出版信息

Pediatr Emerg Care. 2004 Sep;20(9):610-2. doi: 10.1097/01.pec.0000139745.77085.c0.

DOI:10.1097/01.pec.0000139745.77085.c0
PMID:15599265
Abstract

Young infants may present to an emergency department after an acute life-threatening event. The differential diagnosis for an acute life-threatening event is quite extensive. Fortunately, most will have benign or treatable causes. A case of Sturge-Weber syndrome is described in a 2-day old who presented to the emergency department after an acute life-threatening event. A thorough history and detailed physical examination are generally helpful in discerning the etiology for most acute life-threatening events and may at times reveal unusual diseases such as Sturge-Weber syndrome.

摘要

年幼婴儿在发生急性危及生命的事件后可能会被送往急诊科。急性危及生命事件的鉴别诊断范围相当广泛。幸运的是,大多数情况都有良性或可治疗的病因。本文描述了一例2日龄患斯特奇-韦伯综合征的婴儿,该婴儿在发生急性危及生命的事件后被送往急诊科。全面的病史和详细的体格检查通常有助于查明大多数急性危及生命事件的病因,有时可能会发现诸如斯特奇-韦伯综合征等罕见疾病。

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