获得性肝脑变性：一例报告。
Acquired hepatocerebral degeneration: a case report.
作者信息
Chen Wei-Xing, Wang Ping, Yan Sen-Xiang, Li You-Ming, Yu Chao-Hui, Jiang Ling-Ling
机构信息
Department of Gastroenterology, First Affiliated Hospital, College of Medicine, Zhejiang University, 261 Qingchun Road, Hangzhou 310003, Zhejiang Province, China.
出版信息
World J Gastroenterol. 2005 Feb 7;11(5):764-6. doi: 10.3748/wjg.v11.i5.764.
AIM
Acquired hepatocerebral degeneration (AHD) is an exceptional type of hepatic encephalopathies (HE). It is characterized by neuropsychiatric and extrapyramidal symptomatology similar to that seen in hepatolenticular degeneration (Wilson's disease). In this paper, we report a case of AHD with unusual presenting features.
METHODS
A 28-year-old man with AHD was described and the literature was reviewed.
RESULTS
The man had a history of HBV-related liver cirrhosis. He was admitted to our hospital with apathy, dysarthria, mild consciousness impairment and extrapyramidal symptoms after hematemesis. By review of the literature, cases with AHD often did not present consciousness impairment. So our case was once diagnosed incorrectly as Wilson's disease.
CONCLUSION
AHD is a rare syndrome and its variable clinical manifestations make it difficult to be diagnosed. But we believe that extensive examination and thorough understanding of the disease are beneficial to a correct diagnosis. Moreover, biocoene is effective in treating the case.
目的
获得性肝脑变性（AHD）是肝性脑病（HE）的一种特殊类型。其特征为神经精神和锥体外系症状，与肝豆状核变性（威尔逊病）相似。在本文中，我们报告一例具有不寻常表现特征的AHD病例。
方法
描述了一名患有AHD的28岁男性病例，并对文献进行了回顾。
结果
该男性有乙型肝炎相关肝硬化病史。他因呕血后出现淡漠、构音障碍、轻度意识障碍和锥体外系症状而入住我院。通过文献回顾，AHD病例通常不会出现意识障碍。因此，我们的病例曾被误诊为威尔逊病。
结论
AHD是一种罕见综合征，其临床表现多样，难以诊断。但我们认为，进行全面检查并深入了解该疾病有助于正确诊断。此外，生物群落对该病例有效。
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