Yang X, Freeman L J, Ross C
Department of Internal Medicine, Duke University Medical Centre, Durham, North Carolina, USA.
Postgrad Med J. 2005 Feb;81(952):133-4. doi: 10.1136/pgmj.2004.020172.
The case history is described of a man in his 73rd year who was one of the oldest surviving patients with uncorrected tetralogy of Fallot (ToF) before succumbing with renal failure. Factors contributing to his longevity included small pulmonary arteries and presumed slow development of subpulmonary obstruction together with moderate concentric left ventricular hypertrophy--features previously seen in long term survivors. Less than 3% of all patients with uncorrected ToF survive beyond their 40s but late operative repair is still a valuable option. Practicalities of renal dialysis in the presence of an intracardiac shunt are considered.
本文描述了一名73岁男性的病史，他是未经矫正的法洛四联症（ToF）患者中存活时间最长的患者之一，最终死于肾衰竭。他长寿的因素包括肺动脉细小、推测肺下梗阻发展缓慢以及中度同心性左心室肥厚，这些特征以前在长期存活者中可见。所有未经矫正的ToF患者中，不到3%能活到40多岁，但晚期手术修复仍是一个有价值的选择。文中还考虑了存在心内分流时进行肾透析的实际情况。
