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58 岁女性未修复的法洛四联症:观察到的生存的影响因素(病例报告)。

Unrepaired tetralogy of Fallot in a 58-year-old female: factors contributing to the observed survival (case report).

机构信息

Cardiovascular Surgery Department, Hassan II University Hospital, Fez, Morocco.

Faculty of Medicine and Pharmacy, Sidi Mohammed Ben Abdallah University, Fez, Morocco.

出版信息

Pan Afr Med J. 2023 Aug 9;45:154. doi: 10.11604/pamj.2023.45.154.29477. eCollection 2023.

DOI:10.11604/pamj.2023.45.154.29477
PMID:37869227
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10589413/
Abstract

Tetralogy of Fallot (TOF) is the most common form of cyanotic congenital heart disease. Less than 3% of all patients with uncorrected TOF reach their 40 year of life. We present the case of a 58-year-old woman female with uncorrected TOF. The main factors contributing to her longevity are the early development of aortopulmonary collaterals channels and the relatively gradual narrowing of the right ventricular outflow tract.

摘要

法洛四联症(TOF)是最常见的发绀型先天性心脏病。未经矫正的 TOF 患者中,不到 3%的人能活到 40 岁。我们报告了一例未经矫正的 TOF 58 岁女性患者。导致其长寿的主要因素是早期形成的体肺侧支循环以及右心室流出道相对逐渐变窄。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7d01/10589413/0f82b818c537/PAMJ-45-154-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7d01/10589413/69fcd1d8860f/PAMJ-45-154-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7d01/10589413/25fe5a78f2de/PAMJ-45-154-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7d01/10589413/d0eb49a36b32/PAMJ-45-154-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7d01/10589413/d62aaba72487/PAMJ-45-154-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7d01/10589413/0a03fd85bb13/PAMJ-45-154-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7d01/10589413/0f82b818c537/PAMJ-45-154-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7d01/10589413/69fcd1d8860f/PAMJ-45-154-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7d01/10589413/25fe5a78f2de/PAMJ-45-154-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7d01/10589413/d0eb49a36b32/PAMJ-45-154-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7d01/10589413/d62aaba72487/PAMJ-45-154-g004.jpg
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https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7d01/10589413/0f82b818c537/PAMJ-45-154-g006.jpg

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Unrepaired tetralogy of Fallot in a 58-year-old female: factors contributing to the observed survival (case report).58 岁女性未修复的法洛四联症:观察到的生存的影响因素(病例报告)。
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本文引用的文献

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