Godambe Sunit, McNamara Patrick, Rajguru Manju, Hellmann Jonathan
Department of Pediatrics, Hospital for Sick Children, University of Toronto, Toronto, Ontario, Canada.
J Perinatol. 2005 Apr;25(4):289-92. doi: 10.1038/sj.jp.7211250.
Incontinentia pigmenti (Bloch-Sulzberger syndrome) is a multisystem disorder with classical changing skin lesions. The other systems that are involved include the central nervous system, eye, hair, teeth, musculoskeletal system and, occasionally, the cardiovascular system. We report a neonate with a diagnosis of incontinentia pigmenti who presented at birth with pulmonary hypertension. This presentation has not been described in the literature.
色素失禁症(布洛赫-苏尔茨贝格综合征)是一种具有典型皮肤病变变化的多系统疾病。受累的其他系统包括中枢神经系统、眼睛、毛发、牙齿、肌肉骨骼系统,偶尔还包括心血管系统。我们报告了一名诊断为色素失禁症的新生儿,出生时即出现肺动脉高压。这种表现尚未在文献中描述过。