Schaller J, Kock M, Goos M
Klinik und Poliklinik für Dermatologie und Venerologie, Universitätsklinikum Essen.
Hautarzt. 1992 Jun;43(6):383-5.
The case report of a 2-week-old girl suffering from incontinentia pigmenti (Bloch-Sulzberger Syndrome) with disseminated urticarial erythemas, papules and vesicles at the onset is presented. Histological examination showed eosinophilic spongiosis. The peripheral blood eosinophilia and the development of typical lesions led to the diagnosis of incontinentia pigmenti. Eosinophilic spongiosis and peripheral blood eosinophilia are important symptoms in the diagnosis of atypical incontinentia pigmenti.
本文报告了一名2周大患色素失禁症（布洛赫 - 苏尔茨贝格综合征）的女婴病例，起病时出现弥漫性荨麻疹样红斑、丘疹和水疱。组织学检查显示嗜酸性海绵形成。外周血嗜酸性粒细胞增多以及典型皮损的出现导致色素失禁症的诊断。嗜酸性海绵形成和外周血嗜酸性粒细胞增多是不典型色素失禁症诊断中的重要症状。
