Blessing Erwin, Rottbauer Wolfgang, Mereles Derliz, Hosch Waldemar, Benz Andreas, Friess Helmut, Autschbach Frank, Müller Martina, Stremmel Wolfgang, Katus Hugo
Department of Cardiology, University of Heidelberg, Heidelberg, Germany.
J Am Soc Echocardiogr. 2005 Jun;18(6):693. doi: 10.1016/j.echo.2004.08.022.
Isolated noncompaction of the left ventricular (LV) myocardium is a rare congenital disorder resulting from an arrest of the compaction process of the myocardial trabeculae during normal embryogenesis. It is characterized by the presence of prominent LV myocardial trabeculations and deep intertrabecular recesses that are in continuity with the LV cavity. The most common clinical presentation includes progressive LV dysfunction, life-threatening tachyarrhythmias, and the risk for severe cardioembolic events. We describe a case where isolated noncompaction of the LV myocardium was diagnosed after an embolic occlusion of the superior mesenteric artery in a 40-year-old Caucasian woman.
