Baumgart R, Bürklein D, Hinterwimmer S, Thaller P, Mutschler W
Surgical Department University of Munich, Nussbaumstrasse 20, 80336 Munich, Germany.
J Bone Joint Surg Br. 2005 Jul;87(7):1000-4. doi: 10.1302/0301-620X.87B7.16365.
Ollier's disease is characterised by severe deformity of the extremities and retarded growth because of multiple enchondromas. For correction of deformity, the Ilizarov method has been used although it has many complications. A 17-year-old boy with Ollier's disease had a limb-length discrepancy of 17.4 cm, with a valgus deformity of the right knee and recurvatum of the femur of 23 degrees . He had undergone three unsuccessful attempts to correct the deformities by using external fixators. We used a fully implantable, motorised, lengthening and correction nail (Fitbone) to achieve full correction of all the deformities without complications. We decided to carry out the procedure in three stages. First, we lengthened the femur by 3.6 cm and the tibia by 4 cm. We then exchanged the femoral nail for a longer implant and achieved a further 6 cm of length. This reduced the shortening to 3.8 cm. When the boy has finished secondary school we will adjust the remaining discrepancy.
骨软骨瘤病的特征是由于多发性内生软骨瘤导致四肢严重畸形和生长发育迟缓。为了矫正畸形,尽管伊里扎洛夫方法有许多并发症,但仍被采用。一名17岁患有骨软骨瘤病的男孩肢体长度相差17.4厘米,右膝外翻畸形,股骨后凸23度。他曾三次尝试使用外固定器矫正畸形,但均未成功。我们使用了一种完全可植入的、电动的、延长和矫正钉(Fitbone)来实现所有畸形的完全矫正且无并发症。我们决定分三个阶段进行手术。首先,我们将股骨延长3.6厘米,胫骨延长4厘米。然后,我们将股骨钉换成更长的植入物,又延长了6厘米。这将缩短长度减少到3.8厘米。当这个男孩完成中学学业后,我们将调整剩余的长度差异。