Huser Aaron J, Hoellwarth Jason Shih, Coppa Valentino, Feldman David S, Paley Dror
Paley Institute, West Palm Beach, FL 33407, USA.
Children (Basel). 2021 Jun 14;8(6):502. doi: 10.3390/children8060502.
There are multiple forms of enchondromatosis with Ollier's and Maffucci's being the most prevalent types. Limb length discrepancy is a common problem in patients with Ollier's and Maffucci's enchondromatosis. There are multiple reports about lengthening bones in patients with enchondromatosis using external fixators. However, there are no case series regarding the use of implantable lengthening technology. The purpose of this paper is to describe our experience with implantable nail lengthening in patients with enchondromatosis. A retrospective chart and radiographic review of patients with enchondromatosis who underwent implantable nail limb lengthening was performed. Seven patients with 14 bony segments were reviewed. A total of 11/14 lengthenings were completed without difficulty. There were no issues in terms of fixation location in patients with Ollier's disease. One patient with Maffucci's syndrome experienced migration of the nail during two lengthenings due to a combination of intralesional fixation and preconsolidation. One patient with Ollier's disease developed a knee extension contracture requiring manipulation under anesthesia. No other complications were recorded. The use of implantable nail lengthening to resolve limb length discrepancies in patients with Ollier's disease appears to be safe and effective.
内生软骨瘤病有多种形式,其中奥利尔病(Ollier病)和马富西综合征(Maffucci综合征)最为常见。肢体长度差异是奥利尔病和马富西综合征患者的常见问题。有多项关于使用外固定器延长内生软骨瘤病患者骨骼的报道。然而,关于使用可植入延长技术的病例系列报道尚无。本文的目的是描述我们在使用可植入髓内钉延长治疗内生软骨瘤病患者方面的经验。对接受可植入髓内钉肢体延长术的内生软骨瘤病患者进行了回顾性病历和影像学检查。对7例患者的14个骨段进行了评估。总共11/14次延长顺利完成。奥利尔病患者在固定位置方面没有问题。1例马富西综合征患者在两次延长过程中,由于病灶内固定和预巩固的综合作用,髓内钉发生移位。1例奥利尔病患者出现膝关节伸直挛缩,需要在麻醉下进行手法治疗。未记录到其他并发症。使用可植入髓内钉延长术来解决奥利尔病患者的肢体长度差异似乎是安全有效的。