Jain Veena, Gupta R, Parkash H
Department of Prosthodontics, Centre for Dental Education and Research, AIIMS, New Delhi, India.
J Indian Soc Pedod Prev Dent. 2005 Jun;23(2):96-8. doi: 10.4103/0970-4388.16451.
Papillon-Lefevre syndrome is a rare recessive genetic disorder. The clinical manifestations include palmar-plantar hyperkeratosis with precocious rapidly progressive periodontal disease that results in premature exfoliation of primary and permanent dentitions. Patients are often edentulous at an early age. Here is the report of prosthodontic rehabilitation of a case of Papillon-Lefevre syndrome in a 6-year-old child.
掌跖角化-牙周破坏综合征是一种罕见的隐性遗传病。临床表现为掌跖角化伴早熟的快速进展性牙周病，导致乳牙和恒牙过早脱落。患者常在幼年时就无牙。本文报告了一名6岁掌跖角化-牙周破坏综合征患儿的口腔修复治疗情况。
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