脉络膜视网膜回旋状萎缩中的黄斑囊样水肿：荧光素血管造影和光学相干断层扫描评估
Cystoid macular edema in gyrate atrophy of the choroid and retina: a fluorescein angiography and optical coherence tomography evaluation.
作者信息
Oliveira Tâmara L, Andrade Rafael E, Muccioli Cristina, Sallum Juliana, Belfort Rubens
机构信息
Vision Institute-IPEPO, Department of Ophthalmology, Federal University of São Paulo, Brazil.
出版信息
Am J Ophthalmol. 2005 Jul;140(1):147-9. doi: 10.1016/j.ajo.2004.12.083.
PURPOSE
To analyze the importance f optical coherence tomography (OCT) to diagnose the cystoid macular edema in a case of gyrate atrophy.
DESIGN
Observational case report.
METHODS
A 12-year-old boy presenting with gyrate atrophy of the choroid and retina underwent ophthalmologic, clinical, and laboratory tests.
RESULTS
Plasma ornithine level was 735 mumol/l. Fluorescein angiography showed bilateral hyperfluorescence involving the central region of the macula. Optical coherence tomography (OCT) disclosed bilateral intraretinal cysts areas of low reflectivity with occasional high-signal elements bridging the retinal layers and intraretinal thickening.
CONCLUSIONS
Both fluorescein angiography and OCT were helpful to confirm the diagnosis of macular involvement as a complication of gyrate atrophy of the choroid and retina in a patient who presented without any clinical evidence of cystoid macular edema, except a decrease in visual acuity.
目的
分析光学相干断层扫描（OCT）在诊断一例回旋状萎缩患者黄斑囊样水肿中的重要性。
设计
观察性病例报告。
方法
对一名患有脉络膜和视网膜回旋状萎缩的12岁男孩进行眼科、临床和实验室检查。
结果
血浆鸟氨酸水平为735μmol/l。荧光素血管造影显示双侧黄斑中心区域高荧光。光学相干断层扫描（OCT）显示双侧视网膜内囊肿区域低反射率，偶尔有高信号成分连接视网膜各层以及视网膜内增厚。
结论
荧光素血管造影和OCT均有助于确诊黄斑受累，该患者作为脉络膜和视网膜回旋状萎缩的并发症，除视力下降外无任何黄斑囊样水肿的临床证据。
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