Cystoid macular edema secondary to gyrate atrophy in a child treated with sub-tenon injection of triamcinolone acetonide.

Gyrate atrophy (GA) of the fundus is a rare, progressive metabolic disease secondary to the deficiency of the pyridoxal phosphate-dependent enzyme, ornithine aminotransferase. GA may lead to cystoid macular edema (CME) resulting from chronic inflammation. We aimed to report a child case with CME secondary to gyrate atrophy. Herein we presented a GA case treated with posterior sub-Tenon triamcinolone acetonide injection. Optical coherence tomography examination revealed the disappearance of the macular edema that is a vision-threatening complication in GA. The present case showed that the posterior sub-Tenon injection of long acting steroids might be a promising treatment in CME secondary to GA.