Sun Ai-Min, Alhabshan Fahad, Branson Helen, Freedom Robert M, Yoo Shi-Joon
Department of Diagnostic Imaging, The Hospital for Sick Children, University of Toronto, 555 University Ave., M5G 1X8, Toronto, ON, Canada.
Pediatr Radiol. 2005 Dec;35(12):1259-62. doi: 10.1007/s00247-005-1569-5. Epub 2005 Aug 12.
Right aortic arch with isolation of the left subclavian artery is a rare disorder. In this entity, the left subclavian artery has its origin from the pulmonary artery via the ductus arteriosus. We report an infant with an unbalanced atrioventricular septal defect, right aortic arch, bilateral ductus arteriosi and an isolated left subclavian artery. This infant also had chromosome 22q11 deletion. The origin and course of the isolated subclavian artery were well-demonstrated using contrast-enhanced 3-D magnetic resonance angiography. This non-invasive diagnostic modality can accurately reveal detailed mediastinal vascular anatomy in a young infant and allows diagnosis of aberrant vascular connections.
右位主动脉弓伴左锁骨下动脉离断是一种罕见的疾病。在这种情况下,左锁骨下动脉起源于肺动脉,经动脉导管发出。我们报告一例患有不平衡型房室间隔缺损、右位主动脉弓、双侧动脉导管及孤立性左锁骨下动脉的婴儿。该婴儿还存在22q11染色体缺失。使用对比增强三维磁共振血管造影可清晰显示孤立性锁骨下动脉的起源和走行。这种非侵入性诊断方法能够准确揭示幼儿纵隔血管的详细解剖结构,并有助于诊断异常血管连接。