Gnanaraj Lawrence, Skibell Bentley C, Coret-Simon Judith, Halliday William, Forrest Christopher, DeAngelis Dan D
Department of Ophthalmology, The Hospital for Sick Children, University of Toronto, Canada.
Ophthalmic Plast Reconstr Surg. 2005 Nov;21(6):445-7. doi: 10.1097/01.iop.0000189222.20693.ff.
Orbital teratomas are rare embryonic tumors composed of a wide diversity of tissues derived from the three germinal layers. The presenting features include, a healthy newborn with extreme unilateral proptosis; marked stretching of the eyelids over a tense, fluctuating mass, with elongation of the palpebral fissure; enlargement of the bony orbit (two to three times normal size) with subsequent nasal and malar deformities; and transillumination of all or part of the orbital mass. Commonly the eye is normally developed but often vision is not preserved either due to exposure or secondary optic atrophy. The objective in the management of orbital teratoma is to save the eye to encourage orbitofacial development, maintain cosmesis and retain some vision. We report a case of massive congenital orbital teratoma successfully removed by an eyelid-sparing exenteration technique.
眼眶畸胎瘤是一种罕见的胚胎性肿瘤，由来自三个胚层的多种组织构成。其临床表现包括：健康新生儿出现极度单侧眼球突出；眼睑在紧张、波动的肿块上明显伸展，睑裂延长；骨性眼眶增大（为正常大小的两到三倍），随后出现鼻和颧骨畸形；眼眶肿块全部或部分透光。通常眼睛发育正常，但常因暴露或继发性视神经萎缩而无法保留视力。眼眶畸胎瘤治疗的目标是挽救眼球，以促进眶面部发育、保持容貌并保留一定视力。我们报告一例通过保留眼睑的眶内容剜除术成功切除巨大先天性眼眶畸胎瘤的病例。
