Plesa-Skwerer Daniela, Faja Susan, Schofield Casey, Verbalis Alyssa, Tager-Flusberg Helen
Department of Anatomy and Neurobiology, Boston University School of Medicine, Boston, MA 02118, USA.
Am J Ment Retard. 2006 Jan;111(1):15-26. doi: 10.1352/0895-8017(2006)111[15:PFAVEO]2.0.CO;2.
People with Williams syndrome are extremely sociable, empathic, and expressive in communication. Some researchers suggest they may be especially sensitive to perceiving emotional expressions. We administered the Faces and Paralanguage subtests of the Diagnostic Analysis of Nonverbal Accuracy Scale (DANVA2), a standardized measure of emotion recognition for basic emotions to three groups: adolescents and adults with Williams syndrome, age and IQ-matched participants with learning/intellectual disability, and age-matched nonimpaired controls. The Williams syndrome and learning/intellectual disability groups performed significantly worse than the typically developing controls on both subtests, especially on negative emotions. Error analysis indicated the same general pattern of performance across versions and subtests of the DANVA2 for all groups. These findings suggest that emotion recognition is not spared in Williams syndrome.
患有威廉姆斯综合征的人在社交方面极为友善，富有同理心，且在交流中善于表达。一些研究人员认为，他们可能对感知情绪表达格外敏感。我们对三组人群进行了非言语准确性诊断分析量表（DANVA2）中的面部表情和副语言子测试，该量表是一种用于识别基本情绪的标准化情绪识别测量工具。这三组人群分别是：患有威廉姆斯综合征的青少年和成年人、年龄及智商匹配的学习/智力障碍参与者，以及年龄匹配的未受损害对照组。在这两项子测试中，威廉姆斯综合征组和学习/智力障碍组的表现均显著低于正常发育的对照组，尤其是在识别负面情绪方面。错误分析表明，DANVA2的所有版本和子测试中，所有组的表现总体模式相同。这些发现表明，威廉姆斯综合征患者在情绪识别方面并无优势。
