Heller P G, Grinberg A R, Lencioni M, Molina M M, Roncoroni A J
Instituto de Investigaciones Médicas Alfredo Lanari, Universidad de Buenos Aires, Argentina.
Chest. 1992 Aug;102(2):642-3. doi: 10.1378/chest.102.2.642.
Pulmonary arterial hypertension (PAH) and cor pulmonale were found in a patient with paroxysmal nocturnal hemoglobinuria (PNH). Autopsy revealed widespread thromboses in pulmonary microvasculature. Vascular thromboses attributed to hypercoagulability have been found in PNH in many organs, including the lungs. PAH has not been reported, however. This disease should then be considered a rare cause of PAH.
在一名阵发性夜间血红蛋白尿（PNH）患者中发现了肺动脉高压（PAH）和肺心病。尸检显示肺微血管广泛血栓形成。在PNH患者的许多器官（包括肺）中都发现了归因于高凝状态的血管血栓形成。然而，尚未有PAH的相关报道。因此，这种疾病应被视为PAH的一种罕见病因。
