Routsi Christina, Charitos Christos, Rontogianni Demetra, Daniil Zoe, Zakynthinos Epaminondas
Int J Cardiol. 2006 Apr 14;108(3):418-21. doi: 10.1016/j.ijcard.2005.03.062.
An unusual case of fibrosing mediastinitis with obstruction of the inferior and superior left pulmonary veins and severe narrowing of the right pulmonary artery, disclosed after unilateral pulmonary edema, is described. The 18-year-old male patient had a long history of cough, progressive dyspnea and recurrent hemoptysis and the possible diagnosis of "interstitial fibrosis" from a previous lung biopsy. The diagnosis and the pulmonary vessels involvement were suspected after right heart catheterization combined with transesophageal echocardiography and confirmed during urgent thoracotomy and at postmortem examination.
本文描述了一例罕见的纤维性纵隔炎病例，该病例在单侧肺水肿后被发现，伴有左下和左上肺静脉梗阻以及右肺动脉严重狭窄。这位18岁男性患者有长期咳嗽、进行性呼吸困难和反复咯血的病史，先前的肺活检曾可能诊断为“间质性纤维化”。经右心导管检查并结合经食管超声心动图后怀疑有该诊断及肺血管受累情况，在紧急开胸手术时及尸检时得以证实。
