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经皮间隔消融术治疗左心室中部梗阻性肥厚型心肌病:一例报告

Percutaneous septal ablation for left mid-ventricular obstructive hypertrophic cardiomyopathy: a case report.

作者信息

Tengiz Istemihan, Ercan Ertugrul, Alioglu Emin, Turk Ugur O

机构信息

Cardiology Department, Central Hospital, Bayrakli, Izmir, Turkey.

出版信息

BMC Cardiovasc Disord. 2006 Apr 10;6:15. doi: 10.1186/1471-2261-6-15.

DOI:10.1186/1471-2261-6-15
PMID:16606458
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1459201/
Abstract

BACKGROUND

Mid-ventricular obstructive hypertrophic cardiomyopathy (MVOHC) is a rare type of cardiomyopathy. The diagnosis is based on the hourglass appearance on the left ventriculogram and the presence of pressure gradient between apical and basal chamber of the ventriculum on the hemodynamic assessment.

CASE PRESENTATION

The present case represents successful percutaneous treatment with septal ablation to patient with MVOHC associated with systolic anterior motion of the mitral valve and obstruction at both the mid-ventricular and outflow levels.

CONCLUSION

Alcohol septal ablation has been proposed as less invasive alternatives to surgery in patients with MVOHC.

摘要

背景

心室中部梗阻性肥厚型心肌病(MVOHC)是一种罕见的心肌病类型。诊断基于左心室造影呈沙漏样表现以及血流动力学评估显示心室心尖部与基底部之间存在压力阶差。

病例报告

本病例展示了对一名合并二尖瓣收缩期前向运动以及心室中部和流出道水平梗阻的MVOHC患者成功进行经皮间隔消融治疗。

结论

对于MVOHC患者,已提出酒精间隔消融作为比手术侵入性更小的替代治疗方法。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201d/1459201/a7ac797c3257/1471-2261-6-15-5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201d/1459201/ce84d43c98d7/1471-2261-6-15-1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201d/1459201/0bceb74ffc93/1471-2261-6-15-2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201d/1459201/fcf4eb5bc964/1471-2261-6-15-3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201d/1459201/43fa2d5b8104/1471-2261-6-15-4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201d/1459201/a7ac797c3257/1471-2261-6-15-5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201d/1459201/ce84d43c98d7/1471-2261-6-15-1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201d/1459201/0bceb74ffc93/1471-2261-6-15-2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201d/1459201/fcf4eb5bc964/1471-2261-6-15-3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201d/1459201/43fa2d5b8104/1471-2261-6-15-4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/201d/1459201/a7ac797c3257/1471-2261-6-15-5.jpg

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