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Congenital absence of the portal vein in a child with Turner syndrome.

作者信息

Noe Jacob A, Pittman Heather C, Burton Edward M

机构信息

Department of Radiology, University of Tennessee College of Medicine-Chattanooga Branch, Erlanger Health System, Chattanooga, TN 37403, USA.

出版信息

Pediatr Radiol. 2006 Jun;36(6):566-8. doi: 10.1007/s00247-006-0169-3. Epub 2006 Apr 13.

DOI:10.1007/s00247-006-0169-3
PMID:16612647
Abstract

Congenital absence of the portal vein (CAPV) is a rare malformation associated with hepatic encephalopathy and liver function abnormalities. We report a case of a 2-year-old with Turner syndrome, CAPV, and congenital heart malformations.

摘要

相似文献

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Congenital absence of the portal vein in a child with Turner syndrome.
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2
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本文引用的文献

1
Hepatic nodular lesions associated with abnormal development of the portal vein.与门静脉发育异常相关的肝脏结节性病变。
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2
Vascular involvement of the liver in Turner's syndrome.特纳综合征中肝脏的血管受累情况。
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3
Congenital absence of portal vein with multiple hyperplastic nodular lesions in the liver.先天性门静脉缺如伴肝脏多发增生性结节性病变。
阿伯内西畸形：来自印度的单中心经验及文献综述
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Liver transplantation for a patient with Turner syndrome presenting severe portal hypertension: a case report and literature review.为患有严重门静脉高压的特纳综合征患者进行肝移植：病例报告及文献综述
Surg Case Rep. 2016 Dec;2(1):68. doi: 10.1186/s40792-016-0194-x. Epub 2016 Jun 29.
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Congenital absence of the portal vein associated with focal nodular hyperplasia of the liver and congenital heart disease (Abernethy malformation): A case report and literature review.先天性门静脉缺如合并肝局灶性结节性增生及先天性心脏病（阿伯内西畸形）：一例报告并文献复习
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6
Computed tomography and magnetic resonance imaging of multiple focal nodular hyperplasias of the liver with congenital absence of the portal vein in a Chinese girl: case report and review of the literature.中国女孩先天性门静脉缺如合并肝脏多发局灶性结节性增生的计算机断层扫描和磁共振成像：病例报告及文献复习
Eur J Med Res. 2014 Nov 26;19(1):63. doi: 10.1186/s40001-014-0063-7.
7
Congenital absence of the portal vein in a middle-aged man.一名中年男性先天性门静脉缺如。
Surg Radiol Anat. 2011 May;33(4):369-72. doi: 10.1007/s00276-010-0711-8. Epub 2010 Nov 23.
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Insight into congenital absence of the portal vein: is it rare?先天性门静脉缺如的深入探讨：它罕见吗？
World J Gastroenterol. 2008 Oct 21;14(39):5969-79. doi: 10.3748/wjg.14.5969.
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Turner syndrome.特纳综合征
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Extrahepatic portosystemic shunt in congenital absence of the portal vein depicted by time-resolved contrast-enhanced MR angiography.时间分辨对比增强磁共振血管造影显示先天性门静脉缺如时的肝外门体分流。
Pediatr Radiol. 2007 Jul;37(7):706-9. doi: 10.1007/s00247-007-0475-4. Epub 2007 May 11.
J Gastroenterol. 2003;38(3):288-94. doi: 10.1007/s005350300050.
4
Congenital absence of the portal vein and role of liver transplantation in children.儿童门静脉先天性缺如及肝移植的作用
J Pediatr Surg. 2001 Jul;36(7):1026-31. doi: 10.1053/jpsu.2001.24731.
5
Cardiac anomalies associated with congenital absence of the portal vein.与先天性门静脉缺如相关的心脏异常。
Cardiol Young. 1999 Sep;9(5):522-5. doi: 10.1017/s1047951100005485.
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Congenital absence of the portal vein in a boy.
Pediatr Radiol. 1999 Apr;29(4):235-7. doi: 10.1007/s002470050580.
7
Congenital absence of the portal vein: two cases and a proposed classification system for portasystemic vascular anomalies.先天性门静脉缺如：两例报告及门静脉系统血管异常的分类系统建议
J Pediatr Surg. 1994 Sep;29(9):1239-41. doi: 10.1016/0022-3468(94)90812-5.
8
Rare congenital anomaly of the portal vein.
Br J Surg. 1988 Oct;75(10):1038-9. doi: 10.1002/bjs.1800751028.