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Restoration of NADH-oxidation in complex I and complex III deficient fibroblasts by menadione.

作者信息

Wijburg F A, de Groot C J, Feller N, Wanders R J

机构信息

Department of Paediatrics, University Hospital Amsterdam (AMC), The Netherlands.

出版信息

J Inherit Metab Dis. 1991;14(3):293-6. doi: 10.1007/BF01811685.

DOI:10.1007/BF01811685

PMID:1663191

Abstract

摘要

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Restoration of NADH-oxidation in complex I and complex III deficient fibroblasts by menadione.

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本文引用的文献

31P NMR study of improvement in oxidative phosphorylation by vitamins K3 and C in a patient with a defect in electron transport at complex III in skeletal muscle.

Proc Natl Acad Sci U S A. 1984 Jun;81(11):3529-33. doi: 10.1073/pnas.81.11.3529.

Therapy of mitochondrial disorders.

J Inherit Metab Dis. 1987;10 Suppl 1:129-46. doi: 10.1007/BF01812853.

Respiratory chain defects in the mitochondria of cultured skin fibroblasts from three patients with lacticacidemia.

J Clin Invest. 1986 May;77(5):1422-7. doi: 10.1172/JCI112453.

Electron-transfer restoration by vitamin K3 in a complex III-deficient mutant of S. cerevisiae and sequence of the corresponding cytochrome b mutation.

FEBS Lett. 1989 Sep 11;255(1):5-9. doi: 10.1016/0014-5793(89)81050-6.

The toxicity of menadione and mitozantrone in human liver-derived Hep G2 hepatoma cells.

Biochem Pharmacol. 1989 Apr 15;38(8):1247-55. doi: 10.1016/0006-2952(89)90330-4.

Familial NADH: Q1 oxidoreductase (complex I) deficiency: variable expression and possible treatment.

J Inherit Metab Dis. 1989;12 Suppl 2:349-51. doi: 10.1007/BF03335419.

Detection of respiratory chain dysfunction by measuring lactate and pyruvate production in cultured fibroblasts.

J Inherit Metab Dis. 1990;13(3):355-8. doi: 10.1007/BF01799394.

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Restoration of NADH-oxidation in complex I and complex III deficient fibroblasts by menadione.

作者信息

机构信息

出版信息

相似文献

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