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主动脉心室隧道修复术后升主动脉瘤

Ascending aortic aneurysm following aortico-ventricular tunnel repair.

作者信息

Sakurai Manabu, Takahara Yoshiharu, Takeuchi Shigeyasu, Mogi Kenji

机构信息

Division of Cardiovascular Surgery, Funabashi Municipal Medical Center, Funabashi, Chiba, Japan.

出版信息

Jpn J Thorac Cardiovasc Surg. 2006 Apr;54(4):182-4. doi: 10.1007/BF02662477.

DOI:10.1007/BF02662477
PMID:16642928
Abstract

Aortico-left ventricular tunnel is a very rare congenital anomaly. An 18-year-old boy had undergone tunnel closure at 3 years of age. A moderate degree of aortic regurgitation remained postoperatively. Seven years later, aortic valve replacement for aortic regurgitation was performed. Eight years later, the ascending aortic aneurysm had grown to 63 mm in diameter. This dilatation became an operative indication. Ascending aortic replacement was performed with a Dacron graft. Pathological examination of the resected aortic wall revealed cystic medial degeneration. We report a rare case of ascending aortic aneurysm following surgical repair of the aortico-left ventricular tunnel and aortic valve replacement.

摘要

主动脉-左心室隧道是一种非常罕见的先天性异常。一名18岁男孩在3岁时接受了隧道闭合手术。术后仍存在中度主动脉瓣反流。7年后,因主动脉瓣反流进行了主动脉瓣置换术。8年后,升主动脉瘤直径增大至63mm。这种扩张成为手术指征。使用涤纶人工血管进行了升主动脉置换术。切除的主动脉壁病理检查显示中层囊性变性。我们报告了一例主动脉-左心室隧道手术修复及主动脉瓣置换术后发生升主动脉瘤的罕见病例。

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Ascending aortic aneurysm following aortico-ventricular tunnel repair.主动脉心室隧道修复术后升主动脉瘤
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引用本文的文献

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Aorto-Left Ventricular Tunnel: The First Systematic Review of An Uncommon Entity (177 Worldwide Cases from 1965 to 2024).主动脉-左心室隧道:对一种罕见病症的首次系统综述(1965年至2024年全球177例病例)
Rev Cardiovasc Med. 2025 Feb 20;26(2):26005. doi: 10.31083/RCM26005. eCollection 2025 Feb.
2
Ascending Aortic Aneurysm After Repair of Aortico-Left Ventricular Tunnel.主动脉-左心室隧道修复术后升主动脉瘤
Pediatr Cardiol. 2020 Jan;41(1):206-208. doi: 10.1007/s00246-019-02184-2. Epub 2019 Sep 3.
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Aorto-ventricular tunnel.主动脉心室通道

本文引用的文献

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Histopathological grading of ascending aortic aneurysm: comparison of patients with bicuspid versus tricuspid aortic valve.升主动脉瘤的组织病理学分级:二叶式主动脉瓣与三叶式主动脉瓣患者的比较
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Aortico-left ventricular tunnel in fetuses and infants.胎儿和婴儿的主动脉-左心室通道
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