Sakurai Manabu, Takahara Yoshiharu, Takeuchi Shigeyasu, Mogi Kenji
Division of Cardiovascular Surgery, Funabashi Municipal Medical Center, Funabashi, Chiba, Japan.
Jpn J Thorac Cardiovasc Surg. 2006 Apr;54(4):182-4. doi: 10.1007/BF02662477.
Aortico-left ventricular tunnel is a very rare congenital anomaly. An 18-year-old boy had undergone tunnel closure at 3 years of age. A moderate degree of aortic regurgitation remained postoperatively. Seven years later, aortic valve replacement for aortic regurgitation was performed. Eight years later, the ascending aortic aneurysm had grown to 63 mm in diameter. This dilatation became an operative indication. Ascending aortic replacement was performed with a Dacron graft. Pathological examination of the resected aortic wall revealed cystic medial degeneration. We report a rare case of ascending aortic aneurysm following surgical repair of the aortico-left ventricular tunnel and aortic valve replacement.
主动脉-左心室隧道是一种非常罕见的先天性异常。一名18岁男孩在3岁时接受了隧道闭合手术。术后仍存在中度主动脉瓣反流。7年后,因主动脉瓣反流进行了主动脉瓣置换术。8年后,升主动脉瘤直径增大至63mm。这种扩张成为手术指征。使用涤纶人工血管进行了升主动脉置换术。切除的主动脉壁病理检查显示中层囊性变性。我们报告了一例主动脉-左心室隧道手术修复及主动脉瓣置换术后发生升主动脉瘤的罕见病例。