Killampalli Vijay V, Power Dominic, Stirling Alistair J
Spinal Surgery Unit, The Royal Orthopaedic Hospital NHS Trust, Birmingham, West Midlands, UK.
Eur Spine J. 2006 Oct;15 Suppl 5(Suppl 5):621-5. doi: 10.1007/s00586-006-0138-4. Epub 2006 May 20.
Chordoma is a tumour of notochordal origin which usually involves the sacrum or skull base presenting in adulthood. Chordoma in a mobile spinal segment is infrequent and the authors report an extremely rare presentation of L3 chordoma in a child aged 7 years. Although a benign tumour, mobile segment chordoma is more locally aggressive, more likely to metastasise and has a poorer 5 year survival than sacral and clival lesions. Wide surgical excision and reconstruction is the treatment of choice in vertebral chordoma. This case was treated with staged vertebrectomy and fibular strut graft reconstruction and the results of clinical and radiological follow up at 8 years are presented.
脊索瘤是一种起源于脊索的肿瘤，通常发生于成年期，累及骶骨或颅底。发生于可活动脊柱节段的脊索瘤较为罕见，作者报告了一例极为罕见的7岁儿童L3脊索瘤病例。尽管脊索瘤是良性肿瘤，但可活动节段脊索瘤具有更强的局部侵袭性，更易发生转移，与骶骨和斜坡病变相比，其5年生存率更低。广泛手术切除及重建是脊柱脊索瘤的首选治疗方法。该病例采用分期椎体切除术及腓骨支撑植骨重建进行治疗，并展示了8年的临床及影像学随访结果。
