Ohtsuka Takashi, Nomori Hiroaki, Watanabe Ken-Ichi, Kaji Masahiro, Ebihara Akinori, Naruke Tsuguo, Suemasu Keiichi
Department of Thoracic Surgery, Saiseikai Central Hospital, 1-4-17 Mita, Minato-ku, Tokyo, 108-0073, Japan.
Surg Today. 2006;36(6):525-7. doi: 10.1007/s00595-006-3182-0.
Congenital unilateral absence of a pulmonary artery (UAPA) is a rare anomaly usually diagnosed in childhood. We report a case of isolated UAPA in an adult without any other cardiovascular anomaly. The patient was admitted for repeated progressive hemoptysis, which we treated with embolization of the bronchial artery three times, despite which the hemoptysis kept recurring. Finally, the patient was treated successfully by right pneumonectomy. Thus, we think that surgical intervention is indicated for recurrent hemoptysis in patients with isolated UAPA.
先天性单侧肺动脉缺如（UAPA）是一种罕见的异常情况，通常在儿童期被诊断出来。我们报告一例成年患者孤立性UAPA，且无任何其他心血管异常。该患者因反复进行性咯血入院，我们对其进行了三次支气管动脉栓塞治疗，尽管如此，咯血仍反复出现。最后，患者通过右肺切除术成功治愈。因此，我们认为对于孤立性UAPA患者反复咯血，手术干预是必要的。
