Ozgun Niksarlıoğlu Elif Yelda, Yeter Ayse, Cetinkaya Ali, Uysal Mehmet Atilla, Çamsarı Güngör
Department of Chest Disease, Yedikule Chest Diseases and Thoracic Surgery Training and Research Hospital, Istanbul, Turkey.
Respir Med Case Rep. 2017 Jul 15;22:106-108. doi: 10.1016/j.rmcr.2017.07.006. eCollection 2017.
Unilateral hypoplasia of a pulmonary artery (UHPA) is a rare condition that is usually associated with cardiac anomalies in childhood. In the absence of cardiac anomalies, patients may not be diagnosed until respiratory symptoms develop. We present two patients who were diagnosed as having isolated unilateral right pulmonary artery hypoplasia, one a woman aged 80 years, the other, a man aged 55 years. To our knowledge, woman is the oldest patient with UHPA in the English medical literature. Awareness of this condition may contribute to the early recognition of these cases and planning of appropriate treatment.
单侧肺动脉发育不全（UHPA）是一种罕见病症，通常与儿童期心脏异常有关。在没有心脏异常的情况下，患者可能直到出现呼吸道症状才被诊断出来。我们报告了两名被诊断为孤立性单侧右肺动脉发育不全的患者，一名80岁女性，另一名55岁男性。据我们所知，该80岁女性是英文医学文献中年龄最大的单侧肺动脉发育不全患者。认识到这种病症可能有助于早期识别这些病例并规划适当的治疗方案。
