Bekoe S, Pellegrini R V, DiMarco R F, Grant K J, Woelfel G F
Department of Surgery, Mercy Hospital of Pittsburgh, Pennsylvania.
Ann Thorac Surg. 1993 Jun;55(6):1553-4. doi: 10.1016/0003-4975(93)91108-y.
Unilateral absence of pulmonary artery is a rare malformation that can present as an isolated lesion or may be associated with other congenital heart defects. Clinical presentation is subtle when the lesion occurs alone, and may include hemoptysis, which results from rupture of abundant bronchial submucosal vessels perfused by enlarged systemic collaterals that supply the affected lung. Pneumonectomy is recommended as definitive treatment in such an adult patient.
单侧肺动脉缺如是一种罕见的畸形，可表现为孤立性病变，或与其他先天性心脏缺陷相关。当病变单独出现时，临床表现不明显，可能包括咯血，这是由于供应患侧肺的扩张体循环侧支灌注丰富的支气管黏膜下血管破裂所致。对于这样的成年患者，建议行肺切除术作为确定性治疗。
