基于导管的弯刀综合征房间隔缺损封堵术

Catheter-based closure of an atrial septal defect in scimitar syndrome.

作者信息

Odland Hans H, Smevik Bjarne, Bjørnstad Per G

机构信息

Department of Pediatric Cardiology, National Hospital, 0027 Oslo, Norway.

出版信息

Pediatr Cardiol. 2006 Jul-Aug;27(4):500-2. doi: 10.1007/s00246-006-1268-5. Epub 2006 Jul 11.

DOI:10.1007/s00246-006-1268-5

PMID:16835802

Abstract

We report a patient with abnormal systemic blood supply to the right lung and right-sided anomalous pulmonary venous drainage to the inferior vena cava (scimitar syndrome or pulmonary venolobar syndrome). In addition, she had an atrial septal defect, underdeveloped right pulmonary artery, an aberrant right bronchus, and tracheobronchomalacia. She improved markedly after palliative interventional closure of her atrial septal defect.

摘要

我们报告了一名患者，其右肺存在异常的体循环供血，且右侧肺静脉异常引流至下腔静脉（弯刀综合征或肺静脉叶综合征）。此外，她还患有房间隔缺损、右肺动脉发育不全、右支气管异常及气管支气管软化症。在对其房间隔缺损进行姑息性介入封堵术后，她的病情有了显著改善。