Couto Wilson José, Gross Jefferson Luiz, Deheinzelin Daniel, Younes Riad Naim
Departamento de Cirurgia Torácica, Centro de Tratamento e Pesquisa, Hospital do Câncer A.C. Camargo, Rua Prof. Antonio Prudente 211, Liberdade, Cep. 01509-900 São Paulo/SP.
Rev Assoc Med Bras (1992). 2006 May-Jun;52(3):182-6. doi: 10.1590/s0104-42302006000300020. Epub 2006 Jul 10.
Primary mediastinal germ cell tumors account for approximately 10% to 20% of all neoplasms of the mediastinum. It is generally accepted that they represent the malignant transformation of germinal elements without a gonadal focus. These tumors can be classified as teratomas, seminomas, nonseminomatous (yolk sac tumor, embryonal carcinoma, choriocarcinoma) and combined germ-cell tumors without teratomatous components. This review purposes to discuss the different primary mediastinal germ-cell tumors, their clinical presentation and options for treatment.
原发性纵隔生殖细胞肿瘤约占所有纵隔肿瘤的10%至20%。人们普遍认为,它们代表了无性腺病灶的生殖细胞成分的恶性转化。这些肿瘤可分为畸胎瘤、精原细胞瘤、非精原细胞瘤(卵黄囊瘤、胚胎癌、绒毛膜癌)以及无畸胎瘤成分的混合性生殖细胞肿瘤。本综述旨在探讨不同类型的原发性纵隔生殖细胞肿瘤、它们的临床表现及治疗选择。