Seike Y, Nagashima M, Sato H, Hori T, Ishitoya H, Hibino N, Tomino T
Department of Cardiovascular Surgery, Ehime Prefectural Central Hospital, Matsuyama, Japan.
Kyobu Geka. 2006 Jul;59(7):573-6.
A 3-year-old boy suffered from the poor body weight gain under the diagnosis of partial anomalous pulmonary venous connection (PAPVC) to the high portion of the superior vena cava (SVC) associated with ventricular septal defect (VSD) and intact atrial septum (IAS). Preoperative cardiac catheterization revealed the pulmonary to systemic flow ratio 2.6 and mean pulmonary arterial pressure of 21 mmHg. He successfully underwent surgical repair with Williams method using right atrial (RA) flap out and VSD patch closure. Postoperative course was uneventful and echocardiography demonstrated no obstruction at the both routes of neo-SVC and neo-right upper pulmonary venous return.
一名3岁男孩因体重增长缓慢被诊断为部分性肺静脉异位连接（PAPVC），连接至上腔静脉（SVC）高位，合并室间隔缺损（VSD）及完整房间隔（IAS）。术前心脏导管检查显示肺循环与体循环血流量之比为2.6，平均肺动脉压为21 mmHg。他成功接受了Williams法手术修复，采用右心房（RA）瓣片翻转及VSD修补术。术后过程顺利，超声心动图显示新SVC和新右上肺静脉回流两条路径均无梗阻。
