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特发性息肉样脉络膜血管病变(IPCV)。

Idiopathic polypoidal choroidal vasculopathy (IPCV).

作者信息

Yannuzzi L A, Sorenson J, Spaide R F, Lipson B

机构信息

LuEsther T. Mertz Retinal Research Lab, Manhattan Eye, Ear and Throat Hospital, New York, NY 10021.

出版信息

Retina. 1990;10(1):1-8.

PMID:1693009
Abstract

Eleven patients, 40 to 71 years old, had a choroidal vasculopathy that led to hemorrhagic and exudative macular degeneration. The patients had peculiar polypoidal, subretinal, vascular lesions associated with serious and hemorrhagic detachments of the retinal pigment epithelium. This macular disorder, which we have named idiopathic polypoidal choroidal vasculopathy (IPCV), appears to represent a distinct entity that differs clinically and demographically from age-related macular degeneration (AMD) and other macular diseases associated with subretinal neovascularization. Recognition of this condition is important because it may have specific risk factors, natural course, and management considerations that differ from those of age-related macular degeneration.

摘要

11名年龄在40至71岁之间的患者患有脉络膜血管病变,导致出血性和渗出性黄斑变性。这些患者有特殊的息肉样、视网膜下血管病变,伴有视网膜色素上皮的严重出血性脱离。这种黄斑疾病,我们命名为特发性息肉样脉络膜血管病变(IPCV),似乎代表了一种独特的疾病实体,在临床和人口统计学上与年龄相关性黄斑变性(AMD)以及其他与视网膜下新生血管形成相关的黄斑疾病不同。认识到这种疾病很重要,因为它可能有与年龄相关性黄斑变性不同的特定危险因素、自然病程和治疗考量。

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Idiopathic polypoidal choroidal vasculopathy (IPCV).特发性息肉样脉络膜血管病变(IPCV)。
Retina. 1990;10(1):1-8.
2
Idiopathic polypoidal choroidal vasculopathy (IPCV). 1990.特发性息肉样脉络膜血管病变(IPCV)。1990 年。
Retina. 2012 Feb;32 Suppl 1:1-8.
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Indocyanine green videoangiography of idiopathic polypoidal choroidal vasculopathy.特发性息肉状脉络膜血管病变的吲哚菁绿视频血管造影
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[Idiopathic polypoid choroid vasculopathy].
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