Moon Kyung-Sub, Lee Jung-Kil, Kim Jae-Hyoo, Kim Soo-Han
Department of Neurosurgery, Chonnam National University Hospital and Medical School, 8 Hak-dong, Dong-ku, Gwangju, 501-757, South Korea.
Childs Nerv Syst. 2007 Jan;23(1):99-104. doi: 10.1007/s00381-006-0161-0. Epub 2006 Aug 30.
Suprasellar arachnoid cysts are uncommon developmental anomalies that are most often diagnosed in childhood. Because the natural history and pathogenesis of these remain poorly defined, optimal treatment guidelines are not yet established.
We report a case of spontaneous disappearance of a suprasellar arachnoid cyst that persisted after a ventriculoperitoneal shunt performed 10 years earlier. A 5-year-old boy presented with impaired visual acuity and urinary incontinence. Magnetic resonance (MR) imaging showed a large suprasellar cyst with noncommunicating hydrocephalus. A ventriculoperitoneal shunt was put in place to alleviate current aggravation of hydrocephalus symptoms. Because of the persistent size of the cyst and signs of brainstem compression on a repeat computed tomography (CT), we recommended surgical exploration and decompression. However, the boy's parents declined any further surgical treatment, and the patient was subsequently lost to follow-up for 10 years. When the patient returned to our clinic at the age of 15 years, a repeat MR scan showed a complete disappearance of the cyst. His family denied any significant interval history.
This case represents only the third reported case of spontaneous disappearance of a suprasellar arachnoid cyst. We discuss possible mechanisms and clinical characteristics of the disappearance of the arachnoid cyst with review of the literature.
鞍上蛛网膜囊肿是罕见的发育异常,最常在儿童期被诊断出来。由于其自然病史和发病机制仍不清楚,尚未确立最佳治疗指南。
我们报告一例鞍上蛛网膜囊肿自发消失的病例,该囊肿在10年前进行脑室腹腔分流术后持续存在。一名5岁男孩出现视力受损和尿失禁。磁共振成像显示一个巨大的鞍上囊肿伴梗阻性脑积水。进行脑室腹腔分流术以缓解当前脑积水症状的加重。由于囊肿大小持续存在且重复计算机断层扫描显示有脑干受压迹象,我们建议进行手术探查和减压。然而,男孩的父母拒绝任何进一步的手术治疗,随后该患者失访10年。当患者15岁回到我们诊所时,重复磁共振扫描显示囊肿完全消失。其家人否认在此期间有任何重要病史。
本病例是鞍上蛛网膜囊肿自发消失的第三例报告病例。我们通过文献回顾讨论了蛛网膜囊肿消失的可能机制和临床特征。