• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

肺淋巴管平滑肌瘤病。

Pulmonary lymphangioleiomyomatosis.

作者信息

Okimasa Seiji, Shibata Satoshi

机构信息

Division of Thoracic Surgery, Higashi-Hiroshima Medical Center, Japan.

出版信息

Jpn J Thorac Cardiovasc Surg. 2006 Aug;54(8):356-8. doi: 10.1007/s11748-006-0012-7.

DOI:10.1007/s11748-006-0012-7
PMID:16972644
Abstract

We report a case of lymphangioleiomyomatosis (LAM) in a 33-year-old woman. Left pneumothorax was noted during a physical checkup at a local clinic. Multiple bullae in the bilateral lungs were also seen on chest computed tomography. Therefore, she underwent surgery for diagnosis and therapy. A large number of cysts of various sizes were seen in the left pleural cavity, and a cyst located at the lingular region was resected. Histopathological examination of the cyst walls showed a thin rim of abnormal muscle consisting of spindle-shaped cells resembling smooth muscle cells as well as thick, eccentric, or concentric proliferation. The examination described above confirmed the diagnosis of LAM. The patient is currently being followed up on an outpatient basis.

摘要

我们报告一例33岁女性的淋巴管平滑肌瘤病(LAM)。在当地诊所体检时发现左侧气胸。胸部计算机断层扫描还显示双侧肺部有多个肺大疱。因此,她接受了手术以进行诊断和治疗。在左胸腔内可见大量大小不一的囊肿,切除了位于舌叶区域的一个囊肿。囊肿壁的组织病理学检查显示,有一层由类似平滑肌细胞的梭形细胞组成的薄异常肌肉边缘,以及增厚、偏心或同心性增生。上述检查确诊为LAM。该患者目前正在门诊接受随访。

相似文献

1
Pulmonary lymphangioleiomyomatosis.肺淋巴管平滑肌瘤病。
Jpn J Thorac Cardiovasc Surg. 2006 Aug;54(8):356-8. doi: 10.1007/s11748-006-0012-7.
2
From the archives of the AFIP: lymphangioleiomyomatosis: radiologic-pathologic correlation.源自武装部队病理研究所档案:淋巴管平滑肌瘤病:放射学与病理学对照
Radiographics. 2005 May-Jun;25(3):803-28. doi: 10.1148/rg.253055006.
3
Pulmonary lymphangioleiomyomatosis in a 29-year-old woman with bilateral spontaneous pneumothorax: case report.一名29岁双侧自发性气胸女性的肺淋巴管平滑肌瘤病:病例报告
Chang Gung Med J. 2000 Mar;23(3):164-8.
4
[Pulmonary lymphangioleiomyomatosis as a rare cause of recurrent spontaneous pneumothorax].[肺淋巴管平滑肌瘤病作为复发性自发性气胸的罕见病因]
Med Klin (Munich). 2004 Jan 15;99(1):43-6. doi: 10.1007/s00063-004-1008-7.
5
[Pulmonary lymphangioleiomyomatosis as a very rare interstitial lung disease].[肺淋巴管平滑肌瘤病——一种极为罕见的间质性肺疾病]
Pol Arch Med Wewn. 2001 Feb;105(2):157-62.
6
[Pulmonary lymphangioleiomyomatosis: report of one case].[肺淋巴管平滑肌瘤病:1例报告]
Rev Med Chil. 2009 Nov;137(11):1474-7. Epub 2010 Jan 13.
7
An early case of pulmonary lymphangioleiomyomatosis diagnosed by video-assisted thoracoscopic surgery.一例通过电视辅助胸腔镜手术诊断的肺淋巴管平滑肌瘤病早期病例。
Ann Thorac Cardiovasc Surg. 2005 Dec;11(6):405-7.
8
Lymphangioleiomyomatosis: pulmonary and abdominal findings with pathologic correlation.淋巴管平滑肌瘤病:肺部和腹部表现及其病理相关性
Radiographics. 2002 Oct;22 Spec No:S185-98. doi: 10.1148/radiographics.22.suppl_1.g02oc13s185.
9
[Pulmonary lymphangiomyomatosis diagnosed by video-assisted thoracic surgery; report of a case].[经电视辅助胸腔镜手术诊断的肺淋巴管平滑肌瘤病;病例报告]
Kyobu Geka. 2008 Nov;61(12):1078-81.
10
Miliary pulmonary lymphangioleiomyomatosis.粟粒性肺淋巴管平滑肌瘤病。
Am J Respir Crit Care Med. 2013 Apr 15;187(8):e15. doi: 10.1164/rccm.201203-0427IM.

本文引用的文献

1
Survival and disease progression in UK patients with lymphangioleiomyomatosis.英国淋巴管平滑肌瘤病患者的生存情况和疾病进展
Thorax. 2004 Sep;59(9):800-3. doi: 10.1136/thx.2004.023283.
2
Lung transplantation for lymphangioleiomyomatosis.淋巴管平滑肌瘤病的肺移植
J Heart Lung Transplant. 2004 Mar;23(3):301-8. doi: 10.1016/S1053-2498(03)00195-5.
3
Mutation analysis of the TSC1 and TSC2 genes in Japanese patients with pulmonary lymphangioleiomyomatosis.日本肺淋巴管平滑肌瘤病患者TSC1和TSC2基因的突变分析
J Hum Genet. 2002;47(1):20-8. doi: 10.1007/s10038-002-8651-8.
4
Prevalence and clinical characteristics of lymphangioleiomyomatosis (LAM) in patients with tuberous sclerosis complex.结节性硬化症患者中淋巴管平滑肌瘤病(LAM)的患病率及临床特征
Am J Respir Crit Care Med. 2001 Aug 15;164(4):669-71. doi: 10.1164/ajrccm.164.4.2101154.
5
Rare diseases. 1. Lymphangioleiomyomatosis: clinical features, management and basic mechanisms.罕见病。1. 淋巴管平滑肌瘤病:临床特征、管理及基本机制
Thorax. 1999 Mar;54(3):254-64. doi: 10.1136/thx.54.3.254.
6
Evidence that lymphangiomyomatosis is caused by TSC2 mutations: chromosome 16p13 loss of heterozygosity in angiomyolipomas and lymph nodes from women with lymphangiomyomatosis.淋巴管平滑肌瘤病由TSC2基因突变引起的证据:淋巴管平滑肌瘤病女性患者的血管平滑肌脂肪瘤和淋巴结中16号染色体p13杂合性缺失。
Am J Hum Genet. 1998 Apr;62(4):810-5. doi: 10.1086/301804.
7
Pulmonary lymphangioleiomyomatosis: a report of 46 patients including a clinicopathologic study of prognostic factors.肺淋巴管平滑肌瘤病:46例患者报告及预后因素的临床病理研究
Am J Respir Crit Care Med. 1995 Feb;151(2 Pt 1):527-33. doi: 10.1164/ajrccm.151.2.7842216.
8
Lymphangioleiomyomatosis. Clinical course in 32 patients.淋巴管平滑肌瘤病。32例患者的临床病程。
N Engl J Med. 1990 Nov 1;323(18):1254-60. doi: 10.1056/NEJM199011013231807.