Tsai Jeng-Dau, Kuo Huang-Tsung, Chou I-Ching, Chang Jeng-Sheng, Su Bai-Horng
Department of Pediatrics, China Medical University Hospital, Taichung, Taiwan.
Acta Paediatr Taiwan. 2006 Jan-Feb;47(1):34-7.
The vein of Galen aneurysm is a rarely seen congenital intracranial vascular malformation with abnormal aneurysmal dilation of the vein of Galen in neonatal stage. We report a full- term female newborn presented with intractable heart failure, pulmonary artery hypertension, and respiratory distress soon after birth, in whom persistent pulmonary hypertension of newborn was suspected initially. Further study by ultrasound revealed turbulent blood flow in the cerebral vascular lesion in the region of vein of Galen; therefore, secondary pulmonary artery hypertension complicated with 'steal' phenomenon was impressed. With the advancement of diagnostic technique, ultrasound provides a rapid and noninvasive method for diagnosing the condition.
大脑大静脉动脉瘤是一种罕见的先天性颅内血管畸形,在新生儿期大脑大静脉出现异常的动脉瘤样扩张。我们报告一例足月女婴,出生后不久即出现难治性心力衰竭、肺动脉高压和呼吸窘迫,最初怀疑为新生儿持续性肺动脉高压。超声进一步检查发现大脑大静脉区域脑血管病变处有血流紊乱;因此,考虑为继发性肺动脉高压合并“盗血”现象。随着诊断技术的进步,超声为诊断该病提供了一种快速且无创的方法。