原发性滑膜肉瘤
Primary synovial sarcoma.
作者信息
Hartstein Morris E, Silver Frankie-Lynn, Ludwig Olivia J, O'Connor Dennis M
机构信息
Department of Ophthalmology, Saint Louis University Eye Institute, Saint Louis University School of Medicine, St. Louis, Missouri 63104, USA.
出版信息
Ophthalmology. 2006 Nov;113(11):2093-6. doi: 10.1016/j.ophtha.2006.04.037.
PURPOSE
To describe the clinicopathologic and immunohistochemical features and treatment of a rare case of primary synovial sarcoma of the orbit.
DESIGN
Retrospective interventional case report.
PARTICIPANT
A 14-year-old young man with histologically proven synovial sarcoma of the orbit. The diagnosis was confirmed by demonstration of a specific chromosomal translocation by polymerase chain reaction studies.
METHODS
The patient was treated with orbital exenteration and followed up for 18 months at regular intervals.
RESULTS
The tumor was excised completely, and the patient has done well during the initial 1-year follow-up with no sign of recurrence.
CONCLUSIONS
We report the fourth case of synovial sarcoma of the orbit and, at 14 years of age, the youngest patient reported.
目的
描述1例罕见的眼眶原发性滑膜肉瘤的临床病理、免疫组化特征及治疗情况。
设计
回顾性干预病例报告。
研究对象
一名14岁组织学确诊为眼眶滑膜肉瘤的青年男性。聚合酶链反应研究证实存在特定染色体易位，从而确诊。
方法
患者接受眼眶内容剜除术，并定期随访18个月。
结果
肿瘤被完全切除，患者在最初1年的随访中情况良好，无复发迹象。
结论
我们报告了第4例眼眶滑膜肉瘤病例，也是报告中最年轻的患者，年仅14岁。
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