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以尿崩症为表现的韦格纳肉芽肿病。

Wegener's granulomatosis presenting as diabetes insipidus.

作者信息

Dutta P, Hayatbhat M, Bhansali A, Bambery P, Kakar N

机构信息

Department of Endocrinology, Pathology, Postgraduate Institute of Medical Education and Research, Chandigarh, India.

出版信息

Exp Clin Endocrinol Diabetes. 2006 Oct;114(9):533-6. doi: 10.1055/s-2006-924122.

DOI:10.1055/s-2006-924122
PMID:17115352
Abstract

Pituitary gland involvement in Wegener's granulomatosis (WG) occurs most commonly in the form of central diabetes insipidus (CDI). However, CDI as a presenting manifestation of WG is very rare. We report two such cases; one of them had multi-organ involvement at presentation, while other developed it during follow-up. CDI was reversible following cytotoxic drug therapy in one of them.

摘要

垂体受累于韦格纳肉芽肿病(WG)最常见的形式是中枢性尿崩症(CDI)。然而,CDI作为WG的首发表现非常罕见。我们报告两例这样的病例;其中一例在初诊时有多器官受累,而另一例在随访期间出现。其中一例经细胞毒性药物治疗后CDI可逆。

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Wegener's granulomatosis presenting as diabetes insipidus.以尿崩症为表现的韦格纳肉芽肿病。
Exp Clin Endocrinol Diabetes. 2006 Oct;114(9):533-6. doi: 10.1055/s-2006-924122.
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Central diabetes insipidus as the presenting symptom of granulomatosis with polyangiitis.中枢性尿崩症作为肉芽肿性多血管炎的首发症状。
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