Monteiro Marcílio, de Albuquerque Antônio Carlos, Nobre Márcio Costa, Veloso Adriano Teixeira, Mendes Vandete Aguiar, de Souza Filho Lucídio Duarte, da Silva Marcelo José, Bicalho Geraldo Vítor Cardoso
Hospital Santa Casa de Montes Claros, and Acadêmico do 8 período do curso de Medicina da Faculdade Estadual de Montes Claros (UNIMONTES), Brazil.
Arq Neuropsiquiatr. 2006 Sep;64(3A):624-7. doi: 10.1590/s0004-282x2006000400020.
Transspheinoidal meningoencephalocele is a rare presentation of dysraphism of the neural tube. It is characterized by the herniation of the neural tissue through a bony defect in the sphenoid bone. The clinical presentation is variable. It may be assymptomatic or it may include an upper airway obstruction, rhinorrhea, meningitis, hypothalamic dysfunction and optic anomalies. The surgical treatment is controversial. We describe the case of a 7-year-old boy who presented a pulsate structure filling the palate, palate digenesis and hypertelorism. The diagnosis of transsphenoidal transpalatal meningoencephalocele was confirmed by a computerized tomography and a magnetic resonance imaging. The child was operated on by the transpalatal/transspheinoidal approach with a good result.
经蝶窦脑膜脑膨出是神经管闭合不全的一种罕见表现。其特征是神经组织通过蝶骨的骨质缺损疝出。临床表现多样。可能无症状，也可能包括上呼吸道梗阻、鼻漏、脑膜炎、下丘脑功能障碍和视觉异常。手术治疗存在争议。我们描述了一名7岁男孩的病例，他出现了填充腭部的搏动性结构、腭裂和眼距增宽。计算机断层扫描和磁共振成像证实了经蝶窦经腭部脑膜脑膨出的诊断。该患儿通过经腭部/经蝶窦入路进行了手术，效果良好。
