Franco Diogo, Alonso Nivaldo, Ruas Renata, da Silva Freitas Renato, Franco Talita
UFRJ, Praia de Botafogo, Rio de Janeiro 22250-040, Brazil.
Childs Nerv Syst. 2009 Nov;25(11):1455-8. doi: 10.1007/s00381-009-0918-3. Epub 2009 Jun 9.
The aim of this study was to highlight the challenges for early diagnosis and the difficulties observed in surgical treatment of patients with transsphenoidal meningoencephalocele associated with cleft lip and/or palate.
We evaluated six male patients treated over the course of 4 years. Five patients presented encephalic herniation with nonfunctional brain tissue; one of these presented herniation of the pituitary gland and cerebral ventricles.
All the patients received surgical treatment for the cleft lip and/or palate. Only one patient underwent repair of the meningoencephalocele, via nasal endoscopy. There were no postprocedural clinical or surgical complications.
The tendency is to avoid neurosurgery, opting for periodic follow-up with magnetic resonance imaging. In the presence of cleft palate, palatoplasty is essential to protect the meningoencephalocele.
本研究的目的是强调经蝶窦脑膜脑膨出合并唇裂和/或腭裂患者早期诊断的挑战以及手术治疗中观察到的困难。
我们评估了在4年期间接受治疗的6例男性患者。5例患者出现伴有无功能脑组织的脑疝；其中1例出现垂体和脑室疝。
所有患者均接受了唇裂和/或腭裂的手术治疗。仅1例患者通过鼻内镜进行了脑膜脑膨出修复。术后无临床或手术并发症。
倾向于避免神经外科手术，选择磁共振成像定期随访。存在腭裂时，腭裂修复术对于保护脑膜脑膨出至关重要。
