Bernheimer Jonathan, Friedberg Mark, Chan Frandics, Silverman Norman
Division of Pediatric Cardiology, Department of Pediatrics, Lucille Packard Children's Hospital, Stanford University, Stanford, California, USA.
Echocardiography. 2007 Mar;24(3):258-62. doi: 10.1111/j.1540-8175.2007.00383.x.
We describe echocardiography and computerized tomographic imaging findings in the two subtypes of fifth aortic arch in infants. In the first form, the fifth aortic arch creates a systemic to systemic connection extending from the ascending to the descending aorta. When this form appears in isolation, it does not cause hemodynamic disturbance, although associated cardiac lesions, such as aortic coarctation or interruption and patent ductus arteriosus, may influence the clinical presentation. In the second form the fifth aortic arch connects the systemic and pulmonary circulations from persistent connections between the embryological fifth and sixth arches, which may cause significant hemodynamic disturbance from left to right shunting. Although this form has been associated with a wide array of congenital cardiac lesions, this is the first description of 5th aortic arch in association with atrioventricular septal defect and double outlet right ventricle.
我们描述了婴儿第五主动脉弓两种亚型的超声心动图和计算机断层成像结果。在第一种形式中，第五主动脉弓形成了一个从升主动脉延伸至降主动脉的体循环到体循环的连接。当这种形式单独出现时，它不会引起血流动力学紊乱，尽管相关的心脏病变，如主动脉缩窄或中断以及动脉导管未闭，可能会影响临床表现。在第二种形式中，第五主动脉弓通过胚胎学上第五和第六主动脉弓之间的持续连接连接体循环和肺循环，这可能会因左向右分流而导致显著的血流动力学紊乱。尽管这种形式与多种先天性心脏病变有关，但这是首次描述第五主动脉弓与房室间隔缺损和右心室双出口相关的情况。
